Primary Sclerosing Cholangitis (PSC) is a rare and chronic disease that is characterized by inflammation and scarring within the bile ducts, causing them to narrow and, eventually, become completely obstructed. This, in turn, restricts the normal flow of bile, ultimately resulting in liver damage.
There is no known cure or specific treatment for PSC itself. Management primarily focuses on symptom relief and addressing complications. In cases where the disease has significantly advanced, a liver transplant may be the only viable treatment option. However, even with a transplant, some patients can experience a recurrence in the transplanted liver.
It’s important to note that the progression of the disease can vary from person to person. Some individuals deteriorate faster, while others have a slower disease course. Irrespective of the disease’s severity, patients and their families can greatly benefit from the support of those around them. Thus, understanding how PSC affects the patients’ lives proves invaluable.